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Autoimmune pulmonary alveolar proteinosis developed during immunosuppressive treatment in polymyositis with interstitial lung disease: a case report

BACKGROUND: Pulmonary alveolar proteinosis (PAP) is characterized by the accumulation of surfactant proteins within the alveolar spaces. Autoimmune PAP (APAP) caused by elevated levels of GM-CSF autoantibodies (GM-Ab) is very rarely associated with systemic autoimmune disease. Here we report a case...

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Detalles Bibliográficos
Autores principales: Sato, S., Akasaka, K., Ohta, H., Tsukahara, Y., Kida, G., Tsumiyama, E., Kusano, K., Oba, T., Nishizawa, T., Kawabe, R., Yamakawa, H., Amano, M., Matsushima, H., Takada, T.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7132862/
https://www.ncbi.nlm.nih.gov/pubmed/32252718
http://dx.doi.org/10.1186/s12890-020-1110-5