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Autoimmune pulmonary alveolar proteinosis developed during immunosuppressive treatment in polymyositis with interstitial lung disease: a case report
BACKGROUND: Pulmonary alveolar proteinosis (PAP) is characterized by the accumulation of surfactant proteins within the alveolar spaces. Autoimmune PAP (APAP) caused by elevated levels of GM-CSF autoantibodies (GM-Ab) is very rarely associated with systemic autoimmune disease. Here we report a case...
Autores principales: | Sato, S., Akasaka, K., Ohta, H., Tsukahara, Y., Kida, G., Tsumiyama, E., Kusano, K., Oba, T., Nishizawa, T., Kawabe, R., Yamakawa, H., Amano, M., Matsushima, H., Takada, T. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7132862/ https://www.ncbi.nlm.nih.gov/pubmed/32252718 http://dx.doi.org/10.1186/s12890-020-1110-5 |
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