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Liver resection for a congenital intrahepatic portosystemic shunt in a child with hyperammonemia and hypermanganesemia: a case report

BACKGROUND: Congenital portosystemic shunt (CPSS) is a rare malformation that leads to hyperammonemia, hypermanganesemia, and various symptoms. CPSSs are divided into intrahepatic and extrahepatic shunts. In patients with persistent CPSS including an intrahepatic portosystemic shunt (IPSS), early in...

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Detalles Bibliográficos
Autores principales: Takama, Yuichi, Nakamura, Tetsuro, Santo, Kenji, Yoneda, Akihiro
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Springer Berlin Heidelberg 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7165232/
https://www.ncbi.nlm.nih.gov/pubmed/32303849
http://dx.doi.org/10.1186/s40792-020-00838-5