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Mechanical Properties of Human Bronchial Epithelial Cells Expressing Wt- and Mutant CFTR
Cystic fibrosis (CF) is caused by mutations in the gene encoding the cystic fibrosis transmembrane conductance regulator (CFTR). A single recessive mutation, the deletion of phenylalanine 508 (F508del), causes severe CF and resides on 70% of mutant chromosomes. Disorganization of the actin cytoskele...
Autores principales: | Carapeto, Ana P., Vitorino, Miguel V., Santos, João D., Ramalho, Sofia S., Robalo, Tiago, Rodrigues, Mário S., Farinha, Carlos M. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7216210/ https://www.ncbi.nlm.nih.gov/pubmed/32326361 http://dx.doi.org/10.3390/ijms21082916 |
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