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Gingival Hypertrophy in a Child with Hyaline Fibromatosis Syndrome

Hyaline fibromatosis syndrome (HFS) is a rare autosomal recessive genetic disorder characterized by accumulation of hyalinized fibrous tissue with cutaneous, mucosal, osteoarticular, and systemic involvement. The condition is caused by a mutation of ANTXR2 gene that results in a faulty synthesis of...

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Detalles Bibliográficos
Autores principales: Knežević, Predrag, Tarle, Marko, Fratrić, Lucija Ida, Tarle, Antonia, Knežević-Krajina, Hana, Macan, Darko
Formato: Online Artículo Texto
Lenguaje:English
Publicado: University of Zagreb School of Dental Medicine, and Croatian Dental Society - Croatian Medical Association 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7233120/
https://www.ncbi.nlm.nih.gov/pubmed/32523159
http://dx.doi.org/10.15644/asc54/1/8