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Deterioration of muscle force and contractile characteristics are early pathological events in spinal and bulbar muscular atrophy mice

Spinal and bulbar muscular atrophy (SBMA), also known as Kennedy's Disease, is a late-onset X-linked progressive neuromuscular disease, which predominantly affects males. The pathological hallmarks of the disease are selective loss of spinal and bulbar motor neurons, accompanied by weakness, at...

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Detalles Bibliográficos
Autores principales: Gray, Anna L., Annan, Leonette, Dick, James R. T., La Spada, Albert R., Hanna, Michael G., Greensmith, Linda, Malik, Bilal
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Company of Biologists Ltd 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7272358/
https://www.ncbi.nlm.nih.gov/pubmed/32152060
http://dx.doi.org/10.1242/dmm.042424