Odevixibat and partial external biliary diversion showed equal improvement of cholestasis in a patient with progressive familial intrahepatic cholestasis

Untreated progressive familial intrahepatic cholestasis (PFIC) type 2, or bile salt exporter protein deficiency, frequently leads to severe pruritus, impaired growth and progressive liver fibrosis with risk of organ failure. We describe a 15-month-old male patient with severe pruritus diagnosed with...

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Detalles Bibliográficos
Autores principales: Slavetinsky, Christoph, Sturm, Ekkehard
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BMJ Publishing Group 2020
Materias:
Novel Treatment (New Drug/Intervention; Established Drug/Procedure in New Situation)
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7326258/
https://www.ncbi.nlm.nih.gov/pubmed/32601135
http://dx.doi.org/10.1136/bcr-2019-234185

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7326258/
https://www.ncbi.nlm.nih.gov/pubmed/32601135
http://dx.doi.org/10.1136/bcr-2019-234185

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