Mitochondrial Proteome of Affected Glutamatergic Neurons in a Mouse Model of Leigh Syndrome

Defects in mitochondrial function lead to severe neuromuscular orphan pathologies known as mitochondrial disease. Among them, Leigh Syndrome is the most common pediatric presentation, characterized by symmetrical brain lesions, hypotonia, motor and respiratory deficits, and premature death. Mitochon...

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Detalles Bibliográficos
Autores principales: Gella, Alejandro, Prada-Dacasa, Patricia, Carrascal, Montserrat, Urpi, Andrea, González-Torres, Melania, Abian, Joaquin, Sanz, Elisenda, Quintana, Albert
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2020
Materias:
Cell and Developmental Biology
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7399339/
https://www.ncbi.nlm.nih.gov/pubmed/32850799
http://dx.doi.org/10.3389/fcell.2020.00660

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7399339/
https://www.ncbi.nlm.nih.gov/pubmed/32850799
http://dx.doi.org/10.3389/fcell.2020.00660

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