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The Impact of a Slow-Release Large Neutral Amino Acids Supplement on Treatment Adherence in Adult Patients with Phenylketonuria

The gold standard treatment for phenylketonuria (PKU) is a lifelong low-phenylalanine (Phe) diet supplemented with Phe-free protein substitutes. Adherence to therapy becomes difficult after childhood. Supplementing with large neutral amino acids (LNAAs) has been proposed as an alternative medication...

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Detalles Bibliográficos
Autores principales: Burlina, Alessandro P., Cazzorla, Chiara, Massa, Pamela, Loro, Christian, Gueraldi, Daniela, Burlina, Alberto B.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7400920/
https://www.ncbi.nlm.nih.gov/pubmed/32674279
http://dx.doi.org/10.3390/nu12072078