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Systemic AL Amyloidosis: Current Approaches to Diagnosis and Management

AL amyloidosis is characterized by a low-level expansion of an indolent, small plasma cell clone that produces amyloidogenic light chains. Amyloid aggregates or preceding intermediaries cause direct cell damage through their proteotoxicity, and amyloid deposits distort tissue architecture, and, even...

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Detalles Bibliográficos
Autores principales: Fotiou, Despina, Dimopoulos, Meletios Athanasios, Kastritis, Efstathios
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer Health 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7430233/
https://www.ncbi.nlm.nih.gov/pubmed/32885146
http://dx.doi.org/10.1097/HS9.0000000000000454