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Systemic AL Amyloidosis: Current Approaches to Diagnosis and Management
AL amyloidosis is characterized by a low-level expansion of an indolent, small plasma cell clone that produces amyloidogenic light chains. Amyloid aggregates or preceding intermediaries cause direct cell damage through their proteotoxicity, and amyloid deposits distort tissue architecture, and, even...
Autores principales: | , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Wolters Kluwer Health
2020
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7430233/ https://www.ncbi.nlm.nih.gov/pubmed/32885146 http://dx.doi.org/10.1097/HS9.0000000000000454 |