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Cystic Fibrosis Defective Response to Infection Involves Autophagy and Lipid Metabolism

Cystic fibrosis (CF) is a hereditary disease, with 70% of patients developing a proteinopathy related to the deletion of phenylalanine 508. CF is associated with multiple organ dysfunction, chronic inflammation, and recurrent lung infections. CF is characterized by defective autophagy, lipid metabol...

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Detalles Bibliográficos
Autores principales: Mingione, Alessandra, Ottaviano, Emerenziana, Barcella, Matteo, Merelli, Ivan, Rosso, Lorenzo, Armeni, Tatiana, Cirilli, Natalia, Ghidoni, Riccardo, Borghi, Elisa, Signorelli, Paola
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7463682/
https://www.ncbi.nlm.nih.gov/pubmed/32781626
http://dx.doi.org/10.3390/cells9081845