Identification and functional characterization of a novel surfactant protein A2 mutation (p.N207Y) in a Chinese family with idiopathic pulmonary fibrosis

BACKGROUND: Idiopathic pulmonary fibrosis (IPF) is a serious disorder with a high mortality rate worldwide. It is characterized by irreversible scarring of the lung parenchyma resulting from excessive collagen production by proliferating fibroblasts/myofibroblasts. Previous studies have revealed tha...

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Detalles Bibliográficos
Autores principales: Liu, Lv, Qin, Jieli, Guo, Ting, Chen, Ping, Ouyang, Ruoyun, Peng, Hong, Luo, Hong
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2020
Materias:
Original Articles
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7507553/
https://www.ncbi.nlm.nih.gov/pubmed/32602668
http://dx.doi.org/10.1002/mgg3.1393

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7507553/
https://www.ncbi.nlm.nih.gov/pubmed/32602668
http://dx.doi.org/10.1002/mgg3.1393

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