Hermansky-Pudlak syndrome-associated pneumothorax with rapid progression of respiratory failure: a case report

BACKGROUND: Hermansky-Pudlak syndrome (HPS) is an extremely rare disease with pulmonary fibrosis (PF), oculocutaneous albinism, induced platelet dysfunction, and granulomatous colitis. Although patients with HPS-associated PF (HPS-PF) often receive treatment with anti-fibrotic agents, including pirf...

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Detalles Bibliográficos
Autores principales: Kato, Yukari, Kato, Motoyasu, Ihara, Hiroaki, Hayakawa, Eri, Shibayama, Kohei, Miura, Keita, Yamada, Tomoko, Mitsuishi, Yoichiro, Shukuya, Takehito, Ito, Jun, Matsunaga, Takeshi, Sato, Tadashi, Suzuki, Kenji, Takahashi, Kazuhisa
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2020
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7541300/
https://www.ncbi.nlm.nih.gov/pubmed/33023548
http://dx.doi.org/10.1186/s12890-020-01302-8

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7541300/
https://www.ncbi.nlm.nih.gov/pubmed/33023548
http://dx.doi.org/10.1186/s12890-020-01302-8

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