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Dysregulated signalling pathways in innate immune cells with cystic fibrosis mutations

Cystic fibrosis (CF) is one of the most common life-limiting recessive genetic disorders in Caucasians, caused by mutations in the cystic fibrosis transmembrane conductance regulator (CFTR). CF is a multi-organ disease that involves the lungs, pancreas, sweat glands, digestive and reproductive syste...

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Detalles Bibliográficos
Autores principales: Lara-Reyna, Samuel, Holbrook, Jonathan, Jarosz-Griffiths, Heledd H., Peckham, Daniel, McDermott, Michael F.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Springer International Publishing 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7599191/
https://www.ncbi.nlm.nih.gov/pubmed/32367193
http://dx.doi.org/10.1007/s00018-020-03540-9