Nutritional Management and Biochemical Outcomes during the Immediate Phase after Liver Transplant for Methylmalonic Acidemia

Methylmalonic acidemia (MMA) is caused by a deficiency of methyl-malonyl-CoA mutase. It is a multisystemic condition with poor clinical outcomes characterized by frequent metabolic decompensation with acidosis, hyperammonemia and encephalopathy. Restriction of intact protein and supplementation with...

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Detalles Bibliográficos
Autores principales: Siegel, Casey, Arnon, Ronen, Florman, Sander, Bucuvalas, John, Oishi, Kimihiko
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2020
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7599551/
https://www.ncbi.nlm.nih.gov/pubmed/33003354
http://dx.doi.org/10.3390/nu12102976

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7599551/
https://www.ncbi.nlm.nih.gov/pubmed/33003354
http://dx.doi.org/10.3390/nu12102976

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