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Pulmonary hypertension secondary to pulmonary fibrosis: clinical data, histopathology and molecular insights

Pulmonary hypertension (PH) developing secondarily in pulmonary fibrosis (PF) patients (PF-PH) is a frequent co-morbidity. The high prevalence of PH in PF patients is very concerning since the presence of PH is a strong predictor of mortality in PF patients. Until recently, PH was thought to arise s...

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Detalles Bibliográficos
Autores principales: Ruffenach, Grégoire, Hong, Jason, Vaillancourt, Mylène, Medzikovic, Lejla, Eghbali, Mansoureh
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7677848/
https://www.ncbi.nlm.nih.gov/pubmed/33208169
http://dx.doi.org/10.1186/s12931-020-01570-2