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Erdheim–Chester Disease and Acute Myeloid Leukemia with Mutated NPM1 in a Patient with Clonal Hematopoiesis: A Case Report

BACKGROUND: Erdheim–Chester Disease (ECD) is a clonal non-Langerhans histiocytosis, classified as a macrophage-dendritic cell neoplasm in the 2016 WHO classification. The exact cell of origin of ECD is unknown, although some limited evidence suggests that it arises from myeloid progenitors. CASE PRE...

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Detalles Bibliográficos
Autores principales: Papageorgiou, Sotirios G, Divane, Aspasia, Roumelioti, Maria, Kottaridi, Christine, Bouchla, Anthi, Georgakopoulos, Alexandros, Ieremiadou, Fotini, Daraki, Aggeliki, Bazani, Efthymia, Thomopoulos, Thomas P, Chatziioannou, Sofia, Mavrogenis, Andreas, Panayiotidis, Panayiotis, Panayiotides, Ioannis G, Pappa, Vasiliki, Foukas, Periklis G
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Dove 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7678692/
https://www.ncbi.nlm.nih.gov/pubmed/33235460
http://dx.doi.org/10.2147/OTT.S276497