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Vasculitis in Cystic Fibrosis
Cystic fibrosis (CF) is an autosomal-recessive multi-organ disease characterized by airways obstruction, recurrent infections, and systemic inflammation. Vasculitis is a severe complication of CF that affects 2–3% of CF patients and is generally associated with poor prognosis. Various pathogenic mec...
Autores principales: | , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Frontiers Media S.A.
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7690646/ https://www.ncbi.nlm.nih.gov/pubmed/33282799 http://dx.doi.org/10.3389/fped.2020.585275 |