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Vasculitis in Cystic Fibrosis

Cystic fibrosis (CF) is an autosomal-recessive multi-organ disease characterized by airways obstruction, recurrent infections, and systemic inflammation. Vasculitis is a severe complication of CF that affects 2–3% of CF patients and is generally associated with poor prognosis. Various pathogenic mec...

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Detalles Bibliográficos
Autores principales: Sposito, Francesca, McNamara, Paul S., Hedrich, Christian M.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7690646/
https://www.ncbi.nlm.nih.gov/pubmed/33282799
http://dx.doi.org/10.3389/fped.2020.585275