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Nutrient Intake and Nutritional Status in Adult Patients with Inherited Metabolic Diseases Treated with Low-Protein Diets: A Review on Urea Cycle Disorders and Branched Chain Organic Acidemias

Low-protein diets (LPDs) are the main treatment for urea cycle disorders (UCDs) and organic acidemias (OAs). In most cases, LPDs start in childhood and must be continued into adulthood. The improved life expectancy of patients with UCDs and OAs raises the question of their consequences on nutritiona...

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Detalles Bibliográficos
Autores principales: Francini-Pesenti, Francesco, Gugelmo, Giorgia, Lenzini, Livia, Vitturi, Nicola
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7693747/
https://www.ncbi.nlm.nih.gov/pubmed/33138136
http://dx.doi.org/10.3390/nu12113331