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Lymphangioleiomyomatosis: a clinical review

Lymphangioleiomyomatosis (LAM) is a diffuse cystic lung disease. There are two main types of LAM: sporadic, and LAM associated with the tuberous sclerosis complex (TSC), which is caused by mutations in the TSC1 and TSC2 genes. LAM is characterised by cystic lung disease resulting in progressive dysp...

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Detalles Bibliográficos
Autores principales: O'Mahony, Anne M., Lynn, Evelyn, Murphy, David J., Fabre, Aurelie, McCarthy, Cormac
Formato: Online Artículo Texto
Lenguaje:English
Publicado: European Respiratory Society 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7714539/
https://www.ncbi.nlm.nih.gov/pubmed/33304400
http://dx.doi.org/10.1183/20734735.0007-2020