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Chediak-Higashi Syndrome With Epstein-Barr Virus Triggered Hemophagocytic Lymphohistiocytosis: A Case Report

Chediak-Higashi syndrome (CHS) is a rare, autosomal-recessive disorder characterized by oculocutaneous albinism, recurrent bacterial infections, progressive neurologic abnormalities, coagulation defects and a high risk of developing hemophagocytic lymphohistiocytosis characterized by pancytopenia, h...

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Detalles Bibliográficos
Autores principales: Gopaal, Nishant, Sharma, Jagdish N, Agrawal, Vijay, Lora, Sawai S, Jadoun, Laxman S
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7733776/
https://www.ncbi.nlm.nih.gov/pubmed/33329964
http://dx.doi.org/10.7759/cureus.11467