Relationship Between Mitochondrial Structure and Bioenergetics in Pseudoxanthoma elasticum Dermal Fibroblasts

Pseudoxanthoma elasticum (PXE) is a genetic disease considered as a paradigm of ectopic mineralization disorders, being characterized by multisystem clinical manifestations due to progressive calcification of skin, eyes, and the cardiovascular system, resembling an age-related phenotype. Although fi...

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Detalles Bibliográficos
Autores principales: Lofaro, Francesco Demetrio, Boraldi, Federica, Garcia-Fernandez, Maria, Estrella, Lara, Valdivielso, Pedro, Quaglino, Daniela
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2020
Materias:
Cell and Developmental Biology
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7773789/
https://www.ncbi.nlm.nih.gov/pubmed/33392199
http://dx.doi.org/10.3389/fcell.2020.610266

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7773789/
https://www.ncbi.nlm.nih.gov/pubmed/33392199
http://dx.doi.org/10.3389/fcell.2020.610266

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