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The analysis of echocardiographic results in patients suffering from epidermolysis bullosa

INTRODUCTION: Cardiac abnormalities revealed in patients suffering from epidermolysis bullosa (EB) include dilated cardiomyopathy (DC) and aortopathy. DC is a rare but serious complication associated with an increased mortality, predominantly observed in recessive dystrophic EB. Echocardiography is...

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Detalles Bibliográficos
Autores principales: Kurnicka, Katarzyna, Osipowicz, Katarzyna, Dzikowska-Diduch, Olga, Wertheim-Tysarowska, Katarzyna, Kowalewski, Cezary, Pruszczyk, Piotr
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Termedia Publishing House 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7874876/
https://www.ncbi.nlm.nih.gov/pubmed/33603603
http://dx.doi.org/10.5114/ada.2020.102101