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Deciphering the Role of Wnt and Rho Signaling Pathway in iPSC-Derived ARVC Cardiomyocytes by In Silico Mathematical Modeling

Arrhythmogenic Right Ventricular cardiomyopathy (ARVC) is an inherited cardiac muscle disease linked to genetic deficiency in components of the desmosomes. The disease is characterized by progressive fibro-fatty replacement of the right ventricle, which acts as a substrate for arrhythmias and sudden...

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Detalles Bibliográficos
Autores principales: Parrotta, Elvira Immacolata, Procopio, Anna, Scalise, Stefania, Esposito, Claudia, Nicoletta, Giovanni, Santamaria, Gianluca, De Angelis, Maria Teresa, Dorn, Tatjana, Moretti, Alessandra, Laugwitz, Karl-Ludwig, Montefusco, Francesco, Cosentino, Carlo, Cuda, Giovanni
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7923182/
https://www.ncbi.nlm.nih.gov/pubmed/33670616
http://dx.doi.org/10.3390/ijms22042004