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Intrahepatic cholangiocarcinoma in a non-cirrhotic liver in a patient with homozygous ZZ alpha-1 antitrypsin deficiency
Alpha-1 antitrypsin (AAT) deficiency, which is an under-recognised metabolic genetic disorder, is known to cause severe lung disease and liver cirrhosis in about 10%–15% of cases. Patients with AAT deficiency are at a higher risk for developing hepatocellular carcinoma, both in cirrhotic and in non-...
Autores principales: | Vuurberg, Nienke E, Van den Boom, Anne Loes, Van den Heuvel, Marius C, Klaase, Joost M |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BMJ Publishing Group
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7931763/ https://www.ncbi.nlm.nih.gov/pubmed/33658218 http://dx.doi.org/10.1136/bcr-2020-240077 |
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