Desmoplastic Small Round Cell Tumor with “Pure” Spindle Cell Morphology and Novel EWS-WT1 Fusion Transcript: Expanding the Morphological and Molecular Spectrum of This Rare Entity

Background: Desmoplastic small round cell tumor (DSRCT) is a rare pediatric soft tissue neoplasm composed of small round tumor cells with prominent stromal desmoplasia, polyphenotypic differentiation and EWSR1-WT1 gene fusion. We, herein, present a unique case of DSRCT, exhibiting a pure spindle cel...

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Detalles Bibliográficos
Autores principales: Magro, Gaetano, Broggi, Giuseppe, Zin, Angelica, Di Benedetto, Vincenzo, Meli, Mariaclaudia, Di Cataldo, Andrea, Alaggio, Rita, Salvatorelli, Lucia
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8003219/
https://www.ncbi.nlm.nih.gov/pubmed/33803887
http://dx.doi.org/10.3390/diagnostics11030545

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8003219/
https://www.ncbi.nlm.nih.gov/pubmed/33803887
http://dx.doi.org/10.3390/diagnostics11030545

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