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Desmoplastic Small Round Cell Tumor with “Pure” Spindle Cell Morphology and Novel EWS-WT1 Fusion Transcript: Expanding the Morphological and Molecular Spectrum of This Rare Entity
Background: Desmoplastic small round cell tumor (DSRCT) is a rare pediatric soft tissue neoplasm composed of small round tumor cells with prominent stromal desmoplasia, polyphenotypic differentiation and EWSR1-WT1 gene fusion. We, herein, present a unique case of DSRCT, exhibiting a pure spindle cel...
Autores principales: | Magro, Gaetano, Broggi, Giuseppe, Zin, Angelica, Di Benedetto, Vincenzo, Meli, Mariaclaudia, Di Cataldo, Andrea, Alaggio, Rita, Salvatorelli, Lucia |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8003219/ https://www.ncbi.nlm.nih.gov/pubmed/33803887 http://dx.doi.org/10.3390/diagnostics11030545 |
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