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Psychosocial burden and professional and social support in patients with hereditary transthyretin amyloidosis (ATTRv) and their relatives in Italy

BACKGROUND: Hereditary transthyretin amyloidosis (hATTR), alias ATTR variant (ATTRv) is a severe and disabling disease causing sensory and motor neuropathy, autonomic dysfunction, and cardiomyopathy. The progressive decline of patient’s functional autonomy negatively affects the patient’s quality of...

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Detalles Bibliográficos
Autores principales: Magliano, Lorenza, Obici, Laura, Sforzini, Claudia, Mazzeo, Anna, Russo, Massimo, Cappelli, Francesco, Fenu, Silvia, Luigetti, Marco, Tagliapietra, Matteo, Gemelli, Chiara, Leonardi, Luca, Tozza, Stefano, Pradotto, Luca Guglielmo, Citarelli, Giulia, Mauro, Alessandro, Manganelli, Fiore, Antonini, Giovanni, Grandis, Marina, Fabrizi, Gian Maria, Sabatelli, Mario, Pareyson, Davide, Perfetto, Federico, Merlini, Giampaolo, Vita, Giuseppe
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8028211/
https://www.ncbi.nlm.nih.gov/pubmed/33827635
http://dx.doi.org/10.1186/s13023-021-01812-6