Pulmonary Vascular Complications in Hereditary Hemorrhagic Telangiectasia and the Underlying Pathophysiology

In this review, we discuss the role of transforming growth factor-beta (TGF-β) in the development of pulmonary vascular disease (PVD), both pulmonary arteriovenous malformations (AVM) and pulmonary hypertension (PH), in hereditary hemorrhagic telangiectasia (HHT). HHT or Rendu-Osler-Weber disease is...

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Detalles Bibliográficos
Autores principales: Bofarid, Sala, Hosman, Anna E., Mager, Johannes J., Snijder, Repke J., Post, Marco C.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2021
Materias:
Review
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8038106/
https://www.ncbi.nlm.nih.gov/pubmed/33801690
http://dx.doi.org/10.3390/ijms22073471

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8038106/
https://www.ncbi.nlm.nih.gov/pubmed/33801690
http://dx.doi.org/10.3390/ijms22073471

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