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Pulmonary Vascular Complications in Hereditary Hemorrhagic Telangiectasia and the Underlying Pathophysiology

In this review, we discuss the role of transforming growth factor-beta (TGF-β) in the development of pulmonary vascular disease (PVD), both pulmonary arteriovenous malformations (AVM) and pulmonary hypertension (PH), in hereditary hemorrhagic telangiectasia (HHT). HHT or Rendu-Osler-Weber disease is...

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Detalles Bibliográficos
Autores principales:	Bofarid, Sala, Hosman, Anna E., Mager, Johannes J., Snijder, Repke J., Post, Marco C.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2021
Materias:	Review
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8038106/ https://www.ncbi.nlm.nih.gov/pubmed/33801690 http://dx.doi.org/10.3390/ijms22073471

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