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Long term follow-up of the dietary intake in propionic acidemia

Long-term dietary management of Propionic acidemia (PA) includes natural protein restriction, and supplementation with medical formula enriched with leucine (Leu) and free of valine (Val), isoleucine (Ileu), methionine (Met), and threonine (Thr). As PA medical formulas have high leucine content, con...

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Detalles Bibliográficos
Autores principales: Mobarak, A., Stockler, S., Salvarinova, R., Van Karnebeek, C., Horvath, G.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8082257/
https://www.ncbi.nlm.nih.gov/pubmed/33981581
http://dx.doi.org/10.1016/j.ymgmr.2021.100757