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Myocardial strain analysis using cardiac magnetic resonance in patients with calpainopathy

BACKGROUND: Limb–girdle muscular dystrophy (LGMD) is a genetically and clinically heterogeneous group of rare muscular dystrophies. Subtype 2A (LGMD2A) also known as “calpainopathy” is an inherited autosomal recessive gene defect. Cardiac dysfunction is common in several forms of LGMD. Cardiac invol...

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Detalles Bibliográficos
Autores principales: Quick, Silvio, Winkler, Max, Speiser, Uwe, Ibrahim, Karim, Schäfer, Jochen, Linke, Axel, Zhang, Kun, Christoph, Marian, Heidrich, Felix M.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8086059/
https://www.ncbi.nlm.nih.gov/pubmed/33931068
http://dx.doi.org/10.1186/s13023-021-01826-0