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Diminished muscle oxygen uptake and fatigue in spinal muscular atrophy

OBJECTIVE: To estimate muscle oxygen uptake and quantify fatigue during exercise in ambulatory individuals with spinal muscular atrophy (SMA) and healthy controls. METHODS: Peak aerobic capacity (VO(2peak)) and workload (W(peak)) were measured by cardiopulmonary exercise test (CPET) in 19 ambulatory...

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Detalles Bibliográficos
Autores principales: Montes, Jacqueline, Goodwin, Ashley M., McDermott, Michael P., Uher, David, Hernandez, Feliz Marie, Coutts, Kayla, Cocchi, Julia, Hauschildt, Margarethe, Cornett, Kayla M., Rao, Ashwini K., Monani, Umrao R., Ewing Garber, Carol, De Vivo, Darryl C.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8108417/
https://www.ncbi.nlm.nih.gov/pubmed/33788421
http://dx.doi.org/10.1002/acn3.51353