Aortic Dimensions, Biophysical Properties, and Plasma Biomarkers in Children and Adults with Marfan or Loeys-Dietz Syndrome

BACKGROUND: Aortic dilation, stiffening, and dissection are common and potentially lethal complications of Marfan syndrome (MFS) and Loeys-Dietz syndrome (LDS), which involve abnormal transforming growth factor beta (TGF-β) signalling. The relation of aortic dimensions, stiffness, and biomarker leve...

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Detalles Bibliográficos
Autores principales: Cui, Jason Z., Harris, Kevin C., Raedschelders, Koen, Hollander, Zsuzsanna, Potts, James E., De Souza, Astrid, Kiess, Marla, McManus, Bruce M., Bernatchez, Pascal, Raffin, Leslie A., Paine, Heidi, van Breemen, Cornelis, Sandor, George G.S., Esfandiarei, Mitra
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2020
Materias:
Original Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8134910/
https://www.ncbi.nlm.nih.gov/pubmed/34027363
http://dx.doi.org/10.1016/j.cjco.2020.12.018

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8134910/
https://www.ncbi.nlm.nih.gov/pubmed/34027363
http://dx.doi.org/10.1016/j.cjco.2020.12.018

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