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Efficacy of interleukin-1 blockade in Schnitzler’s syndrome without detectable monoclonal gammopathy: a case-based review

Schnitzler’s syndrome (SchS) is a rare autoinflammatory disorder characterized by urticarial rash and monoclonal gammopathy which is currently regarded as IL-1 mediated disease. We present the case of a 21-year-old woman presenting with urticarial rash, arthralgias, and elevated inflammatory markers...

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Detalles Bibliográficos
Autores principales: Bixio, Riccardo, Rossini, Maurizio, Giollo, Alessandro
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Springer International Publishing 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8190012/
https://www.ncbi.nlm.nih.gov/pubmed/33175311
http://dx.doi.org/10.1007/s10067-020-05501-w