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CB(1)R and iNOS are distinct players promoting pulmonary fibrosis in Hermansky–Pudlak syndrome
Hermansky–Pudlak syndrome (HPS) is a rare genetic disorder which, in its most common and severe form, HPS‐1, leads to fatal adult‐onset pulmonary fibrosis (PF) with no effective treatment. We evaluated the role of the endocannabinoid/CB(1)R system and inducible nitric oxide synthase (iNOS) for dual‐...
Autores principales: | Cinar, Resat, Park, Joshua K., Zawatsky, Charles N., Coffey, Nathan J., Bodine, Steven P., Abdalla, Jasmina, Yokoyama, Tadafumi, Jourdan, Tony, Jay, Lindsey, Zuo, Mei Xing G., O'Brien, Kevin J., Huang, Junfeng, Mackie, Ken, Alimardanov, Asaf, Iyer, Malliga R., Gahl, William A., Kunos, George, Gochuico, Bernadette R., Malicdan, May Christine V. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
John Wiley and Sons Inc.
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8255071/ https://www.ncbi.nlm.nih.gov/pubmed/34323400 http://dx.doi.org/10.1002/ctm2.471 |
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