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Case Report: Dexmedetomidine for Intractable Clusters of Myoclonic Jerks and Paroxysmal Sympathetic Hyperactivity in Progressive Encephalomyelitis With Rigidity and Myoclonus

Introduction: Progressive encephalomyelitis with rigidity and myoclonus (PERM) is a severe form of stiff-person spectrum disorder characterized by painful spasms, myoclonic jerks, hyperekplexia, brainstem dysfunction, and dysautonomia, which is sometimes resistant to γ-amino-butyric acid (GABA)-ergi...

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Detalles Bibliográficos
Autores principales: Fujino, Yuzo, Shiga, Kensuke, Hori, Masatoshi, Tamura, Aiko, Iizuka, Takahiro
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8311021/
https://www.ncbi.nlm.nih.gov/pubmed/34322087
http://dx.doi.org/10.3389/fneur.2021.703050