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The role of noninvasive ventilation in the management of type II respiratory failure in patients with myotonic dystrophy

Type 1 myotonic dystrophy (DM1) causes sleep disordered breathing and respiratory failure due to a combination of obstructive sleep apnoea, reduced central drive and respiratory muscle weakness. Noninvasive ventilation (NIV) is commonly used for treating respiratory failure in neuromuscular disease;...

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Detalles Bibliográficos
Autores principales: Rautemaa, Vilma, Roberts, Mark E., Bentley, Andrew, Felton, Timothy W.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: European Respiratory Society 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8311128/
https://www.ncbi.nlm.nih.gov/pubmed/34322542
http://dx.doi.org/10.1183/23120541.00192-2020