Airway Abnormalities in Adult Mucopolysaccharidosis and Development of Salford Mucopolysaccharidosis Airway Score

(1) Background: Mucopolysaccharidoses (MPS) are a heterogeneous group of lysosomal storage disorders caused by the absence of enzymes required for degradation of glycosaminoglycans (GAGs). GAGs deposition in tissues leads to progressive airway narrowing and/or tortuosity. Increased longevity of pati...

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Detalles Bibliográficos
Autores principales: Gadepalli, Chaitanya, Stepien, Karolina M., Sharma, Reena, Jovanovic, Ana, Tol, Govind, Bentley, Andrew
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2021
Materias:
Review
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8347638/
https://www.ncbi.nlm.nih.gov/pubmed/34362059
http://dx.doi.org/10.3390/jcm10153275

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8347638/
https://www.ncbi.nlm.nih.gov/pubmed/34362059
http://dx.doi.org/10.3390/jcm10153275

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