The Nitric Oxide Donor, S-Nitrosoglutathione, Rescues Peroxisome Number and Activity Defects in PEX1G843D Mild Zellweger Syndrome Fibroblasts

Peroxisome biogenesis disorders (PBDs) are a group of metabolic developmental diseases caused by mutations in one or more genes encoding peroxisomal proteins. Zellweger syndrome spectrum (PBD-ZSS) results from metabolic dysfunction caused by damaged or non-functional peroxisomes and manifests as a m...

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Detalles Bibliográficos
Autores principales: Liu, Yidi, Weaver, Ceileigh M., Sen, Yarina, Eitzen, Gary, Simmonds, Andrew J., Linchieh, Lilliana, Lurette, Olivier, Hebert-Chatelain, Etienne, Rachubinski, Richard A., Di Cara, Francesca
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2021
Materias:
Cell and Developmental Biology
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8382563/
https://www.ncbi.nlm.nih.gov/pubmed/34434934
http://dx.doi.org/10.3389/fcell.2021.714710

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8382563/
https://www.ncbi.nlm.nih.gov/pubmed/34434934
http://dx.doi.org/10.3389/fcell.2021.714710

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