Segmental Absence of Intestinal Musculature in a Child with Type IV Ehlers–Danlos Syndrome

Patients with vascular Ehlers–Danlos syndrome (vEDS) have a defect in the formation of type III collagen. This defect puts patients at risk of vascular rupture, uterine rupture, and bowel perforations. The segmental absence of intestinal musculature is a rare histopathologic finding, wherein there i...

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Detalles Bibliográficos
Autores principales: Zeky, Nicole, Short, Celia, Keith, Brent, Craver, Randall D., Zagory, Jessica A.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2021
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8393798/
https://www.ncbi.nlm.nih.gov/pubmed/34438571
http://dx.doi.org/10.3390/children8080680

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8393798/
https://www.ncbi.nlm.nih.gov/pubmed/34438571
http://dx.doi.org/10.3390/children8080680

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