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Segmental Absence of Intestinal Musculature in a Child with Type IV Ehlers–Danlos Syndrome
Patients with vascular Ehlers–Danlos syndrome (vEDS) have a defect in the formation of type III collagen. This defect puts patients at risk of vascular rupture, uterine rupture, and bowel perforations. The segmental absence of intestinal musculature is a rare histopathologic finding, wherein there i...
| Autores principales: | , , , , |
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| Formato: | Online Artículo Texto |
| Lenguaje: | English |
| Publicado: |
MDPI
2021
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| Materias: | |
| Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8393798/ https://www.ncbi.nlm.nih.gov/pubmed/34438571 http://dx.doi.org/10.3390/children8080680 |