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Phenotypic Characterization of Immortalized Chondrocytes from a Desbuquois Dysplasia Type 1 Mouse Model: A Tool for Studying Defects in Glycosaminoglycan Biosynthesis

The complexity of skeletal pathologies makes use of in vivo models essential to elucidate the pathogenesis of the diseases; nevertheless, chondrocyte and osteoblast cell lines provide relevant information on the underlying disease mechanisms. Due to the limitations of primary chondrocytes, immortali...

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Detalles Bibliográficos
Autores principales:	Gramegna Tota, Chiara, Valenti, Beatrice, Forlino, Antonella, Rossi, Antonio, Paganini, Chiara
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2021
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8431031/ https://www.ncbi.nlm.nih.gov/pubmed/34502207 http://dx.doi.org/10.3390/ijms22179304

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