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Non-Invasive Respiratory Assessment in Duchenne Muscular Dystrophy: From Clinical Research to Outcome Measures

Ventilatory failure, due to the progressive wasting of respiratory muscles, is the main cause of death in patients with Duchenne muscular dystrophy (DMD). Reliable measures of lung function and respiratory muscle action are important to monitor disease progression, to identify early signs of ventila...

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Detalles Bibliográficos
Autores principales: Pennati, Francesca, LoMauro, Antonella, D’Angelo, Maria Grazia, Aliverti, Andrea
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8468718/
https://www.ncbi.nlm.nih.gov/pubmed/34575096
http://dx.doi.org/10.3390/life11090947