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Metabolic Control of Patients with Phenylketonuria in a Portuguese Metabolic Centre Comparing Three Different Recommendations

Blood phenylalanine (Phe) is used as the primary marker to evaluate metabolic control. Our study aimed to describe the metabolic control of patients with phenylketonuria (PKU) comparing three different treatment recommendations (European guidelines/US guidelines/Portuguese consensus). This was a ret...

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Detalles Bibliográficos
Autores principales: Kanufre, Viviane, Almeida, Manuela Ferreira, Barbosa, Catarina Sousa, Carmona, Carla, Bandeira, Anabela, Martins, Esmeralda, Rocha, Sara, Guimas, Arlindo, Ribeiro, Rosa, MacDonald, Anita, Pinto, Alex, Rocha, Júlio César
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8469656/
https://www.ncbi.nlm.nih.gov/pubmed/34578995
http://dx.doi.org/10.3390/nu13093118