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Metabolic Control of Patients with Phenylketonuria in a Portuguese Metabolic Centre Comparing Three Different Recommendations
Blood phenylalanine (Phe) is used as the primary marker to evaluate metabolic control. Our study aimed to describe the metabolic control of patients with phenylketonuria (PKU) comparing three different treatment recommendations (European guidelines/US guidelines/Portuguese consensus). This was a ret...
Autores principales: | Kanufre, Viviane, Almeida, Manuela Ferreira, Barbosa, Catarina Sousa, Carmona, Carla, Bandeira, Anabela, Martins, Esmeralda, Rocha, Sara, Guimas, Arlindo, Ribeiro, Rosa, MacDonald, Anita, Pinto, Alex, Rocha, Júlio César |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2021
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8469656/ https://www.ncbi.nlm.nih.gov/pubmed/34578995 http://dx.doi.org/10.3390/nu13093118 |
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