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Emotional behavior and brain anatomy of the mdx52 mouse model of Duchenne muscular dystrophy

The exon-52-deleted mdx52 mouse is a critical model of Duchenne muscular dystrophy (DMD), as it features a deletion in a hotspot region of the DMD gene, frequently mutated in patients. Deletion of exon 52 impedes expression of several brain dystrophins (Dp427, Dp260 and Dp140), thus providing a key...

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Detalles Bibliográficos
Autores principales:	Saoudi, Amel, Zarrouki, Faouzi, Sebrié, Catherine, Izabelle, Charlotte, Goyenvalle, Aurélie, Vaillend, Cyrille
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	The Company of Biologists Ltd 2021
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8476816/ https://www.ncbi.nlm.nih.gov/pubmed/34546327 http://dx.doi.org/10.1242/dmm.049028

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