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Deconstructing progressive inflammatory fibrosis in recessive dystrophic epidermolysis bullosa

Recessive dystrophic epidermolysis bullosa (RDEB) is an inherited blistering skin disease, resulting from biallelic mutations in COL7A1, the gene encoding type VII collagen (C7). At mucocutaneous barriers, tissue integrity relies upon linked extracellular matrix (ECM) proteins forming a physiologic...

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Detalles Bibliográficos
Autor principal: Ebens, Christen L
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8495457/
https://www.ncbi.nlm.nih.gov/pubmed/34515407
http://dx.doi.org/10.15252/emmm.202114864