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Natural History of a Mouse Model Overexpressing the Dp71 Dystrophin Isoform

Dystrophin is a 427 kDa protein that stabilizes muscle cell membranes through interactions with the cytoskeleton and various membrane-associated proteins. Loss of dystrophin as in Duchenne muscular dystrophy (DMD) causes progressive skeletal muscle weakness and cardiac dysfunction. Multiple promoter...

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Detalles Bibliográficos
Autores principales:	Lim, Kenji Rowel Q., Shah, Md Nur Ahad, Woo, Stanley, Wilton-Clark, Harry, Zhabyeyev, Pavel, Wang, Faqi, Maruyama, Rika, Oudit, Gavin Y., Yokota, Toshifumi
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2021
Materias:	Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8657860/ https://www.ncbi.nlm.nih.gov/pubmed/34884423 http://dx.doi.org/10.3390/ijms222312617

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