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Case Report: Anesthetic Management and Electrical Cardiometry as Intensive Hemodynamic Monitoring During Cheiloplasty in an Infant With Enzyme-Replaced Pompe Disease and Preserved Preoperative Cardiac Function

Introduction: Pompe disease is caused by deficiency of the lysosomal enzyme acid α-glucosidase, which results in cardiac and muscular complications that can jeopardize perioperative outcomes. We report a 4-month-old infant with Pompe disease receiving cheiloplasty under general anesthesia with the a...

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Detalles Bibliográficos
Autores principales: Liu, Meng-Chen, Wang, Ming-Tse, Chen, Philip Kuo-Ting, Niu, Dau-Ming, Fan Chiang, Yu-Hsuan, Hsieh, Ming-Hui, Tsai, Hsiao-Chien
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2021
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC8710755/
https://www.ncbi.nlm.nih.gov/pubmed/34966699
http://dx.doi.org/10.3389/fped.2021.729824